Publication
Familial case of oral white sponge nevus - a rare hereditary condition
| Summary: | White sponge nevus (WSN) is an autosomal dominant skin disorder characterized by white, corrugated and diffuse plaques mainly affecting the oral mucosa. The condition has a high penetrance and variable expressivity, but familial reports are uncommon. This report presents a familial case of WSN in which two sisters are affected by the disorder. |
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| Main Authors: | Martins Filho, Paulo Ricardo Saquete |
| Other Authors: | Brasileiro, Bernardo Ferreira; Piva, Marta Rabello; Trento, Cléverson Luciano; Santos, Thiago de Santana |
| Subject: | Leukokeratosis Hereditary mucosal Oral mucosa Nevus Leucoqueratose Mucosa hereditária Mucosa oral Nevos |
| Year: | 2016 |
| Country: | Brazil |
| Document type: | article |
| Access type: | open access |
| Associated institution: | IBICT |
| Language: | English |
| Origin: | Oasisbr |
| Summary: | White sponge nevus (WSN) is an autosomal dominant skin disorder characterized by white, corrugated and diffuse plaques mainly affecting the oral mucosa. The condition has a high penetrance and variable expressivity, but familial reports are uncommon. This report presents a familial case of WSN in which two sisters are affected by the disorder. |
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